2025 ICD-10-CM code I27.21
(Active) Effective Date: N/A Revision Date: N/A Deletion Date: N/A Pulmonary heart disease and diseases of pulmonary circulation - Other secondary pulmonary hypertension Diseases of the circulatory system (I00-I99) Feed
Secondary pulmonary arterial hypertension; a type of pulmonary hypertension caused by another underlying medical condition.
Medical necessity for the diagnosis and management of secondary pulmonary arterial hypertension is established by the presence of symptoms and signs consistent with the diagnosis, supporting diagnostic studies, and the need for medical intervention to alleviate symptoms and improve quality of life. The underlying condition contributing to the PAH also needs to be documented and medically necessary to treat.
Diagnosis and management of secondary pulmonary arterial hypertension, including assessment of the underlying cause, monitoring of disease progression, and treatment to manage symptoms and improve quality of life.This may involve medication management, lifestyle modifications, and referral to specialists as needed.
In simple words: This code means high blood pressure in the lung's blood vessels caused by another health problem.It's important for the doctor to also note what other health problem is causing this.
Secondary pulmonary arterial hypertension (PAH) is a form of pulmonary hypertension where elevated blood pressure in the arteries of the lungs is caused by an underlying condition.This contrasts with primary pulmonary hypertension (I27.0), where the cause is unknown.The code I27.21 specifically indicates secondary PAH and requires documentation of the underlying condition causing the hypertension. This could include conditions such as congenital heart disease, connective tissue disorders, HIV infection, liver disease, or certain drug or toxin exposures.The underlying condition should be coded separately.
Example 1: A 55-year-old female with a history of systemic lupus erythematosus presents with shortness of breath and fatigue.Pulmonary hypertension is diagnosed secondary to her autoimmune disease.I27.21 is used to code the secondary PAH, and M32.1 (systemic lupus erythematosus) is coded separately., A 60-year-old male with a history of chronic obstructive pulmonary disease (COPD) and long-standing hypoxia develops progressively worsening dyspnea.Pulmonary hypertension is diagnosed secondary to COPD and hypoxia.I27.21 is used, and J44.1 (Chronic obstructive pulmonary disease with (acute) lower respiratory infection) is coded separately., A 30-year-old female presents with severe dyspnea and fatigue.She has a history of a congenital heart defect (atrial septal defect) which has not been previously treated and is contributing to pulmonary hypertension.I27.21 is used to code the secondary PAH, and Q21.1 (Atrial septal defect) is coded separately.
Complete documentation is crucial for accurate coding.This should include a clear diagnosis of pulmonary hypertension, supporting evidence of elevated pulmonary artery pressure (e.g., echocardiography, right heart catheterization), and documentation of the underlying medical condition causing the secondary PAH.The severity of the PAH (e.g., based on World Health Organization functional classification) and response to treatment should also be documented.
** This code is used to report secondary pulmonary arterial hypertension specifically.If the type of secondary pulmonary hypertension is unspecified, use I27.20.The 7th character is not applicable for this code.
- Payment Status: Active
- Specialties:Cardiology, Pulmonology
- Place of Service:Office, Hospital Inpatient, Hospital Outpatient