In simple words: This code represents high blood pressure in the arteries of the lungs specifically caused by underlying lung conditions or low oxygen levels. Related lung diseases might include bronchiectasis, cystic fibrosis, interstitial lung disease, pleural effusion, or sleep apnea.

Pulmonary hypertension due to lung diseases and hypoxia. Group 3 pulmonary hypertension. Code also associated lung disease, if known, such as: bronchiectasis (J47.-), cystic fibrosis with pulmonary manifestations (E84.0), interstitial lung disease (J84.-), pleural effusion (J90), sleep apnea (G47.3-).

Example 1: A patient with cystic fibrosis (E84.0) experiences shortness of breath and fatigue. Upon examination, they are diagnosed with pulmonary hypertension, confirmed by right heart catheterization. I27.23 is used to code the pulmonary hypertension, along with E84.0 for the underlying cystic fibrosis., A patient with a history of interstitial lung disease (J84.-) presents with symptoms suggestive of pulmonary hypertension. After diagnostic testing, including echocardiography and right heart catheterization, the diagnosis is confirmed, and I27.23 is used to code the condition., A patient with severe obstructive sleep apnea (G47.3-) is found to have pulmonary hypertension during a sleep study. The pulmonary hypertension is attributed to the sleep apnea, and I27.23 is used to document the diagnosis.

Documentation should include confirmation of pulmonary hypertension through diagnostic testing such as right heart catheterization or echocardiography. The underlying lung disease or hypoxia should also be clearly documented, along with any associated symptoms and treatments.