In simple words: Juvenile dermatomyositis is a condition where a child's muscles and blood vessels become inflamed, causing weakness, stiffness, and a skin rash. It can also affect breathing. Doctors diagnose it through tests like blood work, muscle biopsies, and imaging. Treatment often involves medicine to reduce inflammation and support breathing.

Juvenile dermatomyositis with respiratory involvement is a systemic inflammatory condition affecting blood vessels and muscles, typically presenting with a skin rash and respiratory compromise in children aged 18 and younger.It's an autoimmune disorder characterized by muscle weakness, stiffness, soreness, dysphagia, skin rash (often on eyelids, elbows, knees, knuckles, fingers, and toes), skin ulcerations, subcutaneous calcium deposits, and shortness of breath. Diagnosis involves patient history, physical examination, MRI, muscle enzyme level tests, ESR, ANA, antigen and antibody assays, EMG, and muscle/skin biopsies. Treatment commonly includes corticosteroids (e.g., prednisone) for inflammation, respiratory therapy, and potentially mechanical ventilation, along with immunosuppressants.

Example 1: A 7-year-old presents with progressive muscle weakness, a characteristic heliotrope rash on the eyelids, and difficulty swallowing.Blood tests reveal elevated muscle enzymes (creatine kinase).MRI shows muscle inflammation. A diagnosis of juvenile dermatomyositis with respiratory involvement is made based on these findings and respiratory difficulty., A 10-year-old with juvenile dermatomyositis experiences worsening respiratory symptoms, including shortness of breath and decreased lung capacity. Pulmonary function tests confirm restrictive lung disease.This highlights the respiratory involvement aspect of the condition., A 15-year-old previously diagnosed with juvenile dermatomyositis presents with increased muscle weakness and dysphagia, requiring modification of treatment plan and introduction of respiratory support due to respiratory involvement.

Complete patient history including onset and progression of symptoms (muscle weakness, rash, respiratory symptoms), physical examination findings, results of blood tests (muscle enzymes, ESR, ANA, etc.), imaging studies (MRI), EMG results, muscle and skin biopsy reports, pulmonary function tests (if respiratory involvement is significant), and treatment response documentation.

** This code is specific to juvenile dermatomyositis (onset before age 18) with respiratory involvement.Ensure accurate documentation to support the diagnosis and the severity of respiratory involvement.