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2025 ICD-10-CM code Q16.5

Congenital malformation of inner ear.

Use additional codes to specify the type of hearing loss (e.g., sensorineural, conductive). Do not use this code on the maternal record if the malformation is diagnosed prenatally.

Diagnosis and management of congenital inner ear malformations are medically necessary to evaluate the extent of hearing loss, determine appropriate interventions such as hearing aids or cochlear implants, and provide support services for speech and language development.

In simple words: This code describes a birth defect affecting the inner ear, which is responsible for hearing and balance.

A congenital malformation affecting the inner ear structures, including the membranous labyrinth and the organ of Corti. This condition is present from birth and can lead to hearing impairment.

Example 1: A newborn infant is diagnosed with sensorineural hearing loss. Upon further examination, a malformation of the cochlea is discovered., A child presents with delayed speech development. Diagnostic testing reveals a congenital anomaly of the vestibular system, impacting balance and spatial orientation., An adult with a history of congenital hearing loss undergoes imaging which shows an underdeveloped auditory nerve, consistent with a congenital malformation of the inner ear.

Detailed clinical examination findings, including audiological assessments, imaging studies (MRI, CT scan), and genetic testing if appropriate.

** This code excludes congenital deafness (H90.-) as a primary diagnosis, although they can be reported together if both conditions are present.

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