2025 ICD-10-CM code Q44.7
Other congenital malformations of the liver. This code also includes, if applicable, associated malformations affecting other systems.
Medical necessity for services related to Q44.7 is established by the presence of the congenital liver malformation and the need for diagnostic evaluation, treatment, or management of related complications.
Diagnosis and management of congenital liver malformations falls under the purview of pediatricians, gastroenterologists, and potentially geneticists depending on the specific condition.
- XVII. Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- Other congenital malformations of the digestive system (Q38-Q45)
In simple words: This code represents birth defects affecting the liver, including conditions like Alagille syndrome where the liver doesn't develop normally.
This code encompasses congenital malformations of the liver not otherwise specified, including conditions like Alagille syndrome and other structural or functional anomalies present from birth.
Example 1: A newborn presents with prolonged jaundice and is diagnosed with Alagille syndrome, a multi-system disorder including liver abnormalities. Q44.7 would be used to code the liver malformation., An infant undergoes imaging studies revealing a congenital cyst in the liver not classified elsewhere. Q44.7 would be appropriate for this scenario., A child experiences persistent gastrointestinal issues and is found to have abnormal liver architecture present from birth. Q44.7 would be used to document the malformation.
Documentation should include imaging reports, genetic testing results (if applicable), liver function tests, and clinical findings describing the specific malformation.
** This code should not be used on the maternal record. It is specific to the affected infant.
- Payment Status: Active
- Specialties:Pediatrics, Pediatric Gastroenterology, Medical Genetics
- Place of Service:Inpatient Hospital, Outpatient Hospital, Physician's Office