In simple words: A congenital renal cyst, unspecified, indicates the presence of a simple cyst found in the kidney at the time of birth. It is not acquired later in life and is not associated with more complex cystic kidney diseases.

A cyst present from birth affecting the kidney, not otherwise specified.

Example 1: A newborn infant undergoes a renal ultrasound that incidentally reveals a small, solitary cyst on the left kidney.Since it is present at birth and uncomplicated, the appropriate diagnosis code is Q61.00., During a fetal anomaly scan, a developing fetus is found to have multiple small cysts in both kidneys.In the absence of other associated anomalies or genetic syndromes, this could be coded as Q61.00 at birth., An infant with a family history of cystic kidney disease is evaluated and found to have a solitary renal cyst. As the type of cyst isn't otherwise specified but is congenital, Q61.00 is the correct code.

Documentation should include imaging reports (ultrasound, CT, MRI) confirming the presence and characteristics of the cyst, as well as any associated findings or family history suggestive of genetic cystic kidney diseases.The congenital nature of the cyst should be clearly established.

** Excludes1: acquired cyst of kidney (N28.1) and Potter's syndrome (Q60.6).This code is for use in the context of a congenital condition. It is not applicable to cysts that develop later in life due to other causes. Further evaluation might be required to rule out more complex or syndromic conditions, especially if multiple cysts or other anomalies are present.