2025 ICD-10-CM code Q82.0
Hereditary lymphedema. This condition is a congenital disorder characterized by swelling due to impaired lymphatic drainage.
The medical necessity for services related to hereditary lymphedema stems from the chronic nature of the condition and the potential for complications such as infections, skin changes, and functional impairment.Treatment aims to reduce swelling, manage symptoms, prevent infections and improve the patient's quality of life.
Diagnosis and management of hereditary lymphedema typically involves specialists such as geneticists, pediatricians, and vascular surgeons or lymphedema therapists.They confirm the diagnosis, often through genetic testing, and implement a comprehensive treatment plan that might include compression therapy, manual lymphatic drainage, and, in certain cases, surgical interventions.
- Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- Q82 Other congenital malformations of skin
In simple words: Hereditary lymphedema is a condition present from birth where the body's lymph drainage system doesn't work properly, causing swelling, usually in the legs and feet.
Hereditary lymphedema, also known as Milroy disease, is a congenital disorder characterized by swelling, primarily in the lower limbs, due to an inherited abnormality of the lymphatic system. This leads to an accumulation of lymph fluid in the affected tissues.
Example 1: A newborn infant presents with bilateral swelling of the lower extremities, noticeable since birth. Genetic testing confirms a diagnosis of hereditary lymphedema (Milroy disease)., A young child exhibits persistent, painless swelling in one leg, diagnosed as hereditary lymphedema after ruling out other causes.Management involves regular compression therapy to control the swelling and prevent complications., An adult with a family history of Milroy disease develops lymphedema in their legs. Genetic counseling and appropriate management are recommended for their children to detect and manage the condition early.
Complete medical history detailing the onset and progression of swelling, family history of lymphedema, physical examination findings including the extent and location of edema, results of genetic testing (if performed), imaging studies (such as lymphoscintigraphy), and documentation of any associated complications (e.g., infections).
** Hereditary lymphedema is a chronic condition requiring ongoing management.Patient education on proper skin care, hygiene, and self-management techniques is crucial.Genetic counseling is essential for families affected by this hereditary condition.
- Payment Status: Active
- Specialties:Genetics, Pediatrics, Vascular Surgery, Physical Therapy (Lymphedema Therapy)
- Place of Service:Office, Inpatient Hospital, Outpatient Hospital, Independent Clinic