2025 ICD-10-CM code Q82.2
(Revised) Effective Date: N/A Revision Date: N/A Congenital malformations - Other congenital malformations of skin Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) Feed
Congenital cutaneous mastocytosis, encompassing congenital diffuse cutaneous mastocytosis, congenital maculopapular cutaneous mastocytosis, and congenital urticaria pigmentosa.
Medical necessity for coding Q82.2 is established by the presence of clinical findings consistent with congenital cutaneous mastocytosis, confirmed through appropriate diagnostic testing and documentation of the need for management of the condition.
The clinical responsibility for coding Q82.2 rests with the physician or qualified healthcare professional who diagnoses and manages the patient's condition. This involves a thorough history, physical examination, and potentially further investigations to confirm the diagnosis and rule out other conditions.Appropriate documentation is crucial for accurate coding and billing.
- Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- Other congenital malformations (Q80-Q89)
In simple words: This code describes a rare skin condition present from birth, involving an abnormal buildup of mast cells in the skin.Different types are included, all starting in infancy.It's used for billing and insurance purposes.
Q82.2, Congenital cutaneous mastocytosis, is a billable ICD-10-CM code used to classify congenital forms of mastocytosis affecting the skin.This includes congenital diffuse cutaneous mastocytosis, congenital maculopapular cutaneous mastocytosis, and congenital urticaria pigmentosa. It excludes cutaneous mastocytosis not otherwise specified (D47.01), diffuse cutaneous mastocytosis with onset after the newborn period (D47.01), malignant mastocytosis (C96.2-), systemic mastocytosis (D47.02), and urticaria pigmentosa with onset after the newborn period (D47.01).
Example 1: A newborn infant presents with widespread reddish-brown skin discoloration and multiple blisters consistent with diffuse congenital cutaneous mastocytosis. Q82.2 is used for billing., A child is diagnosed with congenital maculopapular cutaneous mastocytosis characterized by small, raised spots on the skin.Q82.2 accurately reflects this diagnosis., An infant shows symptoms of congenital urticaria pigmentosa, a rare form of mast cell disorder presenting at birth. Q82.2 is applicable.
Detailed medical history including family history, complete physical examination findings with descriptions of skin lesions, laboratory results confirming elevated mast cell counts in skin biopsies (if performed), and imaging studies (if applicable).Documentation should clearly differentiate this congenital form from acquired mastocytosis.
** Further sub-classification may be possible depending on the specific type of congenital cutaneous mastocytosis and associated symptoms. Consult the latest ICD-10-CM guidelines for detailed coding instructions. The diagnosis of congenital cutaneous mastocytosis necessitates thorough clinical evaluation and documentation to ensure accurate code assignment.
- Payment Status: Active
- Specialties:Dermatology, Pediatric Dermatology, Hematology, Oncology
- Place of Service:Office, Hospital (Inpatient and Outpatient),Other clinic settings