2025 ICD-10-CM code Q87.410
(Revised) Effective Date: N/A Revision Date: N/A Congenital malformations, deformations and chromosomal abnormalities - Other congenital malformations Q00-Q99 Feed
Marfan syndrome with aortic dilation.
Medical necessity is established by the confirmed diagnosis of Marfan syndrome and the presence of aortic dilation.Aortic dilation in Marfan syndrome poses significant risks, including dissection and rupture, requiring ongoing monitoring and intervention.
In simple words: Marfan syndrome is an inherited condition affecting connective tissues. It can weaken the main artery carrying blood from the heart (aorta), causing it to widen or bulge. This code refers to Marfan syndrome when this widening, called aortic dilation, occurs.
Marfan syndrome is a genetic disorder that affects the body's connective tissue. This condition weakens the aorta, making it susceptible to dilation and increasing the risk of dissection or rupture. This code specifies Marfan syndrome with the presence of aortic dilation.
Example 1:
Documentation should include supporting diagnostic evidence such as echocardiogram or other imaging studies confirming aortic dilation. Additional documentation might include genetic testing results confirming the diagnosis of Marfan syndrome, and any associated manifestations should also be documented.
** This code is not for use on maternal records.Conditions such as inborn errors of metabolism (E70-E88) are excluded.
- Specialties:Cardiology, Genetics, Pediatrics