2025 ICD-10-CM code E84.0
(Active) Effective Date: N/A Metabolic disorders - Cystic Fibrosis 4 Endocrine, Nutritional and Metabolic Diseases Feed
Cystic fibrosis with pulmonary manifestations.
Medical necessity for services related to CF with pulmonary manifestations should be supported by documentation of the severity of respiratory symptoms, frequency of infections, and impact on the patient's respiratory function.
Physicians diagnosing and managing CF should perform thorough clinical evaluations including patient history, physical examination, laboratory tests (such as sweat chloride test, genetic testing for CFTR gene mutations), and imaging studies.Treatment strategies may involve medications to thin mucus, antibiotics to combat infections, airway clearance techniques, and other supportive therapies.
In simple words: Cystic fibrosis (CF) is a genetic condition where the body produces thick, sticky mucus that clogs the lungs and airways, making it hard to breathe and increasing the risk of lung infections. CF can also affect other organs like the pancreas, liver, and intestines. This code specifies that the person with CF is experiencing lung problems.
Cystic fibrosis (CF) is a genetic disorder affecting the exocrine glands, causing the production of abnormally thick and sticky mucus. In the lungs, this mucus obstructs airways, leading to breathing difficulties and increased susceptibility to infections. CF can also impact other organs like the pancreas, liver, intestines, sinuses, and reproductive system.Pulmonary manifestations are a defining characteristic of CF, resulting in respiratory complications.
Example 1: A 10-year-old patient with a confirmed diagnosis of cystic fibrosis presents with persistent cough, shortness of breath, and increased sputum production. The patient has a history of recurrent respiratory infections.Code E84.0 is used to indicate the pulmonary manifestations of CF., A young adult with cystic fibrosis experiences worsening lung function, requiring hospitalization for intravenous antibiotic treatment and respiratory support. Code E84.0 captures the primary reason for admission., An infant with meconium ileus at birth undergoes diagnostic testing, which confirms cystic fibrosis. Despite the initial intestinal manifestation, the code E84.0 is used if pulmonary manifestations are present or become evident during the course of the disease.
Documentation should include details of pulmonary function tests, imaging results, history of respiratory infections, and other clinical findings related to the respiratory system. Any associated infections should be documented with the appropriate ICD-10-CM codes.
- Payment Status: Active
- Specialties:Pulmonology, Pediatrics, Gastroenterology, Genetic Counseling
- Place of Service:Inpatient Hospital, Outpatient Hospital, Physician's Office, Home Health