2025 ICD-10-CM code E84.19
(Active) Effective Date: N/A Cystic fibrosis with intestinal manifestations - Metabolic disorders 4 Endocrine, nutritional and metabolic diseases Feed
Cystic fibrosis with other intestinal manifestations. This code is used for patients with cystic fibrosis who have intestinal complications other than meconium ileus.
Medical necessity for services related to E84.19 is established by the presence of cystic fibrosis and the specific intestinal manifestations that require medical intervention. This can include managing malabsorption, treating DIOS, or addressing complications like pancreatitis.Documentation should support the need for the services provided.
Diagnosis of cystic fibrosis with other intestinal manifestations involves a combination of patient history, physical exam, and laboratory/diagnostic tests.Patient history may reveal symptoms such as greasy stools, weight loss, and constipation.Laboratory tests may include blood tests for immunoreactive trypsinogen, stool tests for chymotrypsin, sputum culture, and a chloride sweat test. Genetic testing for the CFTR gene mutation is also crucial for diagnosis. Treatment is multifaceted and can include medications like Ivacaftor, Lumacaftor, or Tezacaftor to target the underlying genetic defect. Other treatments include pancreatic enzyme supplements to aid nutrient absorption, feeding tubes, intestinal lavage, and potentially surgery for persistent intestinal obstruction.
- 4 Endocrine, nutritional and metabolic diseases
- E84 Cystic fibrosis with intestinal manifestationsE84.1 Cystic fibrosis with other intestinal manifestationsE84.19 Cystic fibrosis with other intestinal manifestations
In simple words: This code is used when someone with cystic fibrosis has problems with their intestines, like trouble absorbing food, but not a specific problem called meconium ileus that newborns can have.
Cystic fibrosis (CF) is an autosomal recessive inherited disorder characterized by the buildup of thick mucus, which can obstruct various organs, including the intestines.In the intestines, this thick mucus can block ducts carrying digestive enzymes, leading to malabsorption of nutrients. This can cause a range of symptoms, including smelly and greasy stools, weight loss, constipation, and in severe cases, can lead to complications like pancreatitis, intestinal obstruction, diabetes, liver disease, and nutritional deficiencies.Code E84.19 specifically refers to intestinal manifestations of CF *other than* meconium ileus (E84.11).
Example 1: A 5-year-old patient with a known history of cystic fibrosis presents with frequent, foul-smelling, greasy stools, abdominal pain, and failure to thrive.Upon examination, the physician determines the symptoms are due to malabsorption related to CF and documents "cystic fibrosis with intestinal manifestations".The correct code is E84.19., A teenager with cystic fibrosis experiences episodes of severe constipation and abdominal distension. Diagnostic imaging reveals distal intestinal obstruction syndrome (DIOS). The appropriate code is E84.19., A young adult with CF presents with recurrent pancreatitis, determined to be a complication of their CF.In this case, while pancreatitis is a significant finding, the underlying CF with intestinal manifestation is coded as E84.19.
Documentation should clearly state the presence of cystic fibrosis and the specific intestinal manifestations observed.This could include symptoms (greasy stools, abdominal pain, distension, constipation), diagnostic findings (imaging results indicating DIOS), or complications like pancreatitis related to the CF.It's important to differentiate from meconium ileus, which has its own code (E84.11). Genetic test results confirming CFTR mutations are also valuable documentation.
- Payment Status: Active
- Specialties:Gastroenterology, Pulmonology, General Practice, Pediatrics
- Place of Service:Inpatient Hospital, Outpatient Hospital, Office, Independent Clinic