2025 ICD-10-CM code E84.9
(Active) Effective Date: N/A Genetic Disorder - Metabolic disorders (E70-E88) Endocrine, Nutritional and Metabolic Diseases (E00-E89) Feed
Cystic fibrosis, unspecified. This code is used when the provider does not document the specific type of CF or any specific manifestations.
Medical necessity for services related to CF depends on the severity of the disease and its impact on the patient's respiratory, digestive, and other systems.Documentation should clearly establish the need for interventions such as medication, airway clearance therapies, and other treatments.
Diagnosis of cystic fibrosis involves evaluating patient history, signs and symptoms, and conducting a physical exam. Laboratory studies include blood tests (immunoreactive trypsinogen), stool tests (chymotrypsin), sputum culture, and a chloride sweat test.Newborn screening and genetic testing (CFTR gene mutation) are also used. Treatment focuses on managing symptoms and may include airway clearance techniques, medications (bronchodilators, mucolytics, antibiotics, pancreatic enzymes), and in some cases, lung transplantation.
- Endocrine, Nutritional and Metabolic Diseases (E00-E89)
- E84 Cystic fibrosis E84.0 Cystic fibrosis with pulmonary manifestations E84.1 Cystic fibrosis with intestinal manifestations E84.8 Cystic fibrosis with other manifestations E84.9 Cystic fibrosis, unspecified
In simple words: Cystic fibrosis (CF) is a genetic condition that causes the body to produce thick, sticky mucus. It primarily affects the lungs, pancreas, and other organs.This particular code is used when the doctor doesn't specify what type of CF it is or what problems it's causing.
Cystic fibrosis is an autosomal recessive inherited disorder that causes a buildup of thick mucus, primarily affecting the lungs, pancreas, liver, intestines, sinuses, and sex organs.This code (E84.9) is used when the provider does not document the specific type of CF or any specific manifestations.
Example 1: A patient presents with chronic cough, recurrent lung infections, and shortness of breath, but the specific type of cystic fibrosis is not yet determined. E84.9 is used until further testing confirms the subtype., A newborn infant is screened for CF and the test is positive, but further testing is required to determine the specific type of CF and its manifestations.E84.9 is used initially., A patient with a family history of CF presents with symptoms suggestive of the condition, but the specific type and manifestations are not documented by the provider during the initial encounter.E84.9 is appropriate in this scenario.
Documentation should include details of the patient's symptoms, family history, physical examination findings, and results of diagnostic tests (sweat chloride test, genetic testing, etc.).
** Cystic fibrosis affects multiple organ systems, and associated conditions (e.g., diabetes, pancreatic insufficiency) may require additional codes.
- Payment Status: Active
- Specialties:Pulmonology, Gastroenterology, Genetics, Pediatrics
- Place of Service:Inpatient Hospital, Outpatient Hospital, Physician's Office, Independent Clinic, Federally Qualified Health Center