2025 ICD-10-CM code G10
(Active) Effective Date: N/A Diseases of the nervous system - G10-G14 6 Feed
Huntington's disease (HD) is a progressive neurodegenerative disorder characterized by uncontrolled movements, cognitive decline, and psychiatric symptoms.
Medical necessity for services related to Huntington's disease should be documented based on the specific needs of the individual. This can include medication management for chorea and psychiatric symptoms, therapy to address functional limitations, genetic counseling, and supportive care to manage disease progression.
Diagnosis and management of Huntington's disease typically involves neurologists, psychiatrists, geneticists, physical therapists, occupational therapists, speech-language pathologists, and other healthcare professionals to address the multifaceted nature of the disease. Genetic testing is crucial for confirming the diagnosis.Treatment focuses on managing symptoms and providing supportive care to improve quality of life.Medications can be used to address chorea, psychiatric symptoms, and other associated issues.Therapy, such as physical, occupational, and speech therapy, can help maintain functional abilities and independence.
In simple words: Huntington's disease is a genetic brain disorder passed down through families.It causes parts of the brain to break down over time, leading to problems with movement, thinking, and emotions.People with Huntington's disease may develop jerky, uncontrolled movements, have trouble with memory and concentration, and experience changes in their personality and mood.There is currently no cure, but treatments are available to help manage symptoms.
Huntington's disease (HD), also known as Huntington's chorea, is an inherited disorder caused by a mutation in the HTT gene, leading to progressive degeneration of nerve cells in the brain. This degeneration primarily affects the basal ganglia and cerebral cortex, resulting in a triad of motor, cognitive, and psychiatric symptoms.Motor symptoms include chorea (involuntary, jerky movements), dystonia (muscle rigidity and contractions), impaired coordination and balance, difficulty walking, dysphagia (trouble swallowing), and slurred speech. Cognitive symptoms involve difficulty organizing, prioritizing, and focusing on tasks, impaired decision-making, memory loss, slowed processing speed, and difficulty learning new information. Psychiatric symptoms can include depression, irritability, apathy, anxiety, obsessive-compulsive disorder, mania, and bipolar disorder. The age of onset typically ranges from 30 to 50 years (adult-onset HD), but can occur in childhood or adolescence (juvenile HD) with a different presentation and more rapid progression.Symptoms worsen over time, ultimately leading to severe functional decline and dependence.
Example 1: A 45-year-old individual presents with involuntary jerking movements in their arms and legs, difficulty concentrating, and increasing irritability. After a thorough evaluation, including genetic testing, a diagnosis of adult-onset Huntington's disease is confirmed., A 15-year-old adolescent exhibits declining school performance, behavioral changes, and stiffness in their gait.Genetic testing reveals a diagnosis of juvenile Huntington's disease., A 60-year-old individual with a family history of Huntington's disease develops progressive difficulty with walking, swallowing, and speaking, along with cognitive decline and depression, consistent with late-onset Huntington's disease.
Documentation should include detailed neurological and psychiatric evaluations, genetic testing results, family history, symptom descriptions (motor, cognitive, and psychiatric), functional assessments, and response to treatment.
- Specialties:Neurology, Psychiatry, Genetics
- Place of Service:Office, Inpatient Hospital, Outpatient Hospital, Skilled Nursing Facility, Nursing Facility, Hospice,Home Health