2025 ICD-10-CM code I42.4
Endocardial fibroelastosis. Congenital cardiomyopathy.
Medical necessity for services related to endocardial fibroelastosis must be established by demonstrating the impact of the condition on the patient's cardiac function and overall health. The diagnostic workup and treatment are necessary to confirm the diagnosis, manage symptoms, improve heart function, prevent complications, and improve the patient's quality of life.
Diagnosis and management of endocardial fibroelastosis typically falls under the purview of pediatric cardiologists or cardiologists specializing in congenital heart disease. They are responsible for diagnosing the condition, usually through echocardiography or cardiac MRI, and developing a treatment plan to manage symptoms and improve heart function. This may involve medications to help the heart pump more efficiently, or in severe cases, surgical intervention like heart transplantation.
In simple words: Endocardial fibroelastosis is a heart condition present from birth where the inner lining of the heart becomes abnormally thick, especially in the main pumping chamber. This can make it harder for the heart to pump blood effectively.
Endocardial fibroelastosis is a condition characterized by thickening of the inner lining of the heart, the endocardium. This thickening primarily affects the left ventricle and can lead to impaired heart function. It's often congenital, meaning present at birth. Elastomyofibrosis is sometimes associated with endocardial fibroelastosis.
Example 1: A newborn infant presents with signs of heart failure, such as rapid breathing and difficulty feeding. An echocardiogram reveals a thickened endocardium in the left ventricle, leading to a diagnosis of endocardial fibroelastosis., A child experiences shortness of breath and fatigue during physical activity. Further examination and imaging lead to a diagnosis of endocardial fibroelastosis, a condition they've had since birth but which has become more symptomatic as they've grown., A young adult is found to have reduced heart function during a routine check-up. Imaging shows a thickened endocardium, and after further evaluation, they are diagnosed with endocardial fibroelastosis, which had gone undetected throughout their childhood.
Documentation should include the diagnostic imaging results (echocardiogram, cardiac MRI) confirming the characteristic thickening of the endocardium and any associated findings such as chamber dilation or reduced heart function. Medical records should also detail the patient's presenting symptoms, such as shortness of breath, fatigue, or signs of heart failure, which prompted further investigation. Any treatment plan, including medications or surgical interventions, should be clearly documented.
- Specialties:pediatric cardiology
- Place of Service:Inpatient Hospital, On Campus-Outpatient Hospital, Office