2025 ICD-10-CM code M30.1
(Active) Effective Date: N/A Revision Date: N/A Deletion Date: N/A Systemic connective tissue disorders - Systemic connective tissue disorders (M30-M36) Diseases of the musculoskeletal system and connective tissue (M00-M99) Feed
Polyarteritis with lung involvement, also known as Churg-Strauss syndrome, is an inflammation of small arteries and veins.
Medical necessity for the diagnosis and treatment of Churg-Strauss syndrome is established through documentation supporting the presence of symptoms and laboratory and imaging findings consistent with the diagnosis.The treatment plan should be tailored to the severity and specific manifestations of the disease and should follow established guidelines for vasculitis management.Documentation of medical necessity is crucial for reimbursement.
Diagnosis and treatment of polyarteritis nodosa with lung involvement requires a multidisciplinary approach, typically involving rheumatologists, pulmonologists, and potentially other specialists depending on the organ systems affected.The physician's responsibilities include obtaining a detailed history, conducting a physical examination, ordering and interpreting laboratory and imaging tests, performing or overseeing biopsies, establishing a diagnosis, developing and implementing a treatment plan, monitoring treatment response, and managing complications.
- Diseases of the musculoskeletal system and connective tissue (M00-M99)
- Systemic connective tissue disorders (M30-M36)
In simple words: Churg-Strauss syndrome is a rare disease causing inflammation in the small blood vessels throughout the body. It often starts with asthma or other lung problems and can cause symptoms like fever, fatigue, weight loss, cough, and pain in the joints or muscles. Doctors use blood tests and imaging (like X-rays or CT scans) to diagnose it.Treatment usually involves medications to reduce inflammation and suppress the immune system.
Polyarteritis nodosa with lung involvement (Churg-Strauss syndrome) is a systemic vasculitis characterized by inflammation of small- and medium-sized arteries and veins.It's associated with eosinophilia and often presents with respiratory symptoms (asthma, cough, shortness of breath), along with systemic manifestations like fever, weight loss, fatigue, peripheral neuropathy, and gastrointestinal issues. Diagnosis involves a combination of clinical presentation, laboratory tests (elevated white blood cell count, eosinophilia, elevated inflammatory markers), imaging studies (chest X-ray, CT scan), and potentially a tissue biopsy. Treatment usually involves corticosteroids to manage inflammation and immunosuppressants like cyclophosphamide to control the immune system's attack on blood vessels.
Example 1: A 45-year-old patient presents with worsening asthma, persistent cough, and fatigue.Laboratory tests reveal eosinophilia and elevated inflammatory markers.Chest CT scan shows pulmonary infiltrates.A tissue biopsy confirms the diagnosis of Churg-Strauss syndrome., A 38-year-old patient with a history of asthma experiences new-onset weakness in their extremities and abdominal pain.Diagnostic workup including blood tests and imaging reveals polyangiitis with involvement of peripheral nerves and mesenteric vessels.The patient is diagnosed with Churg-Strauss syndrome and requires both immunosuppressive and supportive treatment., A 52-year-old patient with a long-standing history of allergic rhinitis and asthma develops severe shortness of breath and purpura. Investigations show eosinophilia and evidence of vasculitis. A renal biopsy confirms renal involvement, and the patient is diagnosed with Churg-Strauss syndrome with renal compromise. The physician coordinates specialized care with nephrology to manage the kidney involvement.
Detailed patient history including respiratory symptoms (asthma, cough, dyspnea), systemic symptoms (fever, weight loss, fatigue, peripheral neuropathy, gastrointestinal problems), and any previous diagnoses. Results of complete blood count (CBC) with differential, inflammatory markers (ESR, CRP), serological tests, chest X-ray, CT scan, and possibly tissue biopsy reports.Documentation of treatment plan and response to therapy.Any complications arising from the disease or treatment should also be documented.
- Payment Status: Active
- Specialties:Rheumatology, Pulmonology, Nephrology
- Place of Service:Office, Hospital Inpatient, Hospital Outpatient