2025 ICD-10-CM code M33.09
(Valid) Effective Date: N/A Revision Date: N/A Diseases of the musculoskeletal system and connective tissue - Systemic connective tissue disorders Diseases of the musculoskeletal system and connective tissue (M00-M99) Feed
Juvenile dermatomyositis with other organ involvement is a systemic inflammatory condition affecting muscles and blood vessels in children under 18, accompanied by a skin rash and other organ-specific symptoms.It is an autoimmune disorder.
Medical necessity for the evaluation and management of juvenile dermatomyositis is established by the presence of signs and symptoms suggestive of the condition, such as muscle weakness, characteristic skin rash, and other organ-specific manifestations.The medical record should document the clinical findings and rationale for diagnostic testing and treatment.
Physicians diagnose juvenile dermatomyositis based on the patient’s history, physical exam, imaging studies (such as MRI), blood tests (to measure muscle enzymes, inflammation markers, and antibodies), electromyography (EMG), and biopsies of muscle and skin tissue. Treatment typically involves corticosteroids to reduce inflammation and medications that suppress the immune system.
- Diseases of the musculoskeletal system and connective tissue (M00-M99)
- M33.0: Juvenile dermatomyositis with other organ involvementM33: DermatopolymyositisM30-M36: Systemic connective tissue disordersM00-M99: Diseases of the musculoskeletal system and connective tissue
In simple words: Juvenile dermatomyositis is a disease that causes inflammation in the muscles and blood vessels of children. It also causes a skin rash.This specific code is used when a child with this condition also has problems with other organs in their body, in addition to their muscles and skin.
Juvenile dermatomyositis with other organ involvement is a systemic inflammatory condition of the muscles and blood vessels that occurs with a skin rash in children 18 years of age or younger, due to an autoimmune disorder. The provider documents a type of organ involvement not represented by another code.Symptoms may include weakness, stiffness and soreness of the muscles, difficulty swallowing, skin rash, skin ulcerations, calcium deposits under the skin and shortness of breath. Other symptoms depend on the organ involved. Diagnosis is based on patient history, physical examination, imaging (MRI), blood tests (muscle enzymes, erythrocyte sedimentation rate, antinuclear antibodies, antigen assays, specific antibody assays), electromyography (EMG), and muscle and skin biopsies. Treatment includes corticosteroids (e.g., prednisone) for inflammation and immunosuppressant drugs.
Example 1: A 12-year-old girl presents with muscle weakness, a distinctive rash around her eyes and knuckles, and difficulty swallowing. After thorough examination and testing, she is diagnosed with juvenile dermatomyositis with esophageal involvement., A 7-year-old boy experiences progressive muscle weakness, skin rash, and shortness of breath.Further investigation reveals interstitial lung disease, confirming a diagnosis of juvenile dermatomyositis with pulmonary involvement., A 15-year-old girl with known juvenile dermatomyositis develops abdominal pain and gastrointestinal symptoms. Diagnostic tests reveal involvement of the small intestine, indicating juvenile dermatomyositis with gastrointestinal involvement.
Documentation should include details of the patient's history, physical findings (including the location and characteristics of the rash), results of laboratory tests (including muscle enzyme levels, inflammatory markers, and autoantibody tests), imaging studies (such as MRI), EMG findings, and biopsy results if performed.The specific organ involvement (other than skin and muscle) should be clearly documented.
- Payment Status: Active
- Specialties:Pediatric Rheumatology, Dermatology, Neurology
- Place of Service:Inpatient Hospital, Outpatient Hospital, Office