2025 ICD-10-CM code Q25.3
(Active) Effective Date: N/A Revision Date: N/A Deletion Date: N/A Congenital malformations - Congenital malformations of the circulatory system Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) Feed
Supravalvular aortic stenosis, a narrowing of the aorta above the aortic valve.
Medical necessity for treatment of supravalvular aortic stenosis is established based on the presence of significant symptoms (e.g., shortness of breath, chest pain, fainting), reduced exercise tolerance, and evidence of significant hemodynamic compromise as demonstrated by echocardiography or cardiac catheterization.The severity of the stenosis and the patient's overall clinical condition guide treatment decisions.
Cardiologists, pediatric cardiologists, and cardiovascular surgeons are primarily responsible for the diagnosis, treatment, and management of supravalvular aortic stenosis.The specific clinical responsibilities depend on the severity of the condition and the chosen treatment approach (e.g., medication, surgery, or catheterization).
- Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- Congenital malformations of the circulatory system (Q20-Q28)
In simple words: Supravalvular aortic stenosis means the aorta, the main artery carrying blood from the heart, is narrower than normal just above the heart valve. This makes it harder for the heart to pump blood to the body.
Q25.3, Supravalvular aortic stenosis, is an ICD-10-CM code that describes a congenital narrowing of the aorta above the aortic valve. This condition affects the aorta's ability to effectively pump blood throughout the body.The narrowing can vary in severity, leading to a range of symptoms and complications.It's important to note that this code excludes congenital aortic stenosis not otherwise specified (Q23.0) and congenital stenosis of the aortic valve (Q23.0).
Example 1: A newborn infant presents with cyanosis (bluish discoloration of the skin) and difficulty breathing. Echocardiography reveals significant narrowing of the aorta above the aortic valve, consistent with supravalvular aortic stenosis.The infant undergoes surgical intervention to widen the narrowed section of the aorta., A 5-year-old child experiences recurrent episodes of fainting and shortness of breath during physical activity. Cardiac evaluation reveals moderate supravalvular aortic stenosis.The child is managed medically with medications to improve heart function and reduce symptoms, avoiding surgery at this stage., A teenager experiences chest pain and dizziness.Cardiac catheterization confirms severe supravalvular aortic stenosis.The patient undergoes a balloon angioplasty to widen the narrowed section of the aorta and improve blood flow.
Complete medical history, including family history of congenital heart defects.Physical examination findings (e.g., heart murmur, cyanosis).Echocardiogram results showing the location and severity of the aortic stenosis.Results of cardiac catheterization (if performed).Details of surgical intervention (if performed), including the type of procedure and postoperative course.Any associated medical conditions.
** This code is used for congenital supravalvular aortic stenosis.It is crucial to differentiate this from other types of aortic stenosis based on location and etiology.
- Payment Status: Active
- Specialties:Cardiology, Pediatric Cardiology, Cardiovascular Surgery
- Place of Service:Inpatient Hospital, Outpatient Hospital, Ambulatory Surgical Center