2025 ICD-10-CM code Q33.4
(Active) Effective Date: N/A Revision Date: N/A Deletion Date: N/A Congenital malformations - Congenital malformations of the respiratory system Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) Feed
Congenital bronchiectasis is a condition where the bronchi (airways in the lungs) are abnormally widened, present from birth.
Medical necessity for diagnosis and treatment of congenital bronchiectasis is established by the presence of symptoms (cough, wheezing, recurrent infections) and confirmation of the diagnosis through imaging and pulmonary function tests.Treatment is medically necessary to manage symptoms, prevent complications, and improve respiratory function.
Pulmonologists, pediatricians, and other respiratory specialists are typically responsible for the diagnosis and management of congenital bronchiectasis.The care may involve regular monitoring of lung function, treatment of infections, and potentially, surgical interventions in severe cases.
- Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- Q30-Q34 (Congenital malformations of the respiratory system)
In simple words: Congenital bronchiectasis is a condition where the airways in a baby's lungs are abnormally wide from birth. This can cause breathing problems and frequent lung infections.
Q33.4, Congenital bronchiectasis, in the ICD-10-CM classification, denotes a congenital anomaly characterized by the abnormal widening of the bronchi (airways in the lungs). This widening is present at birth and can lead to various respiratory problems.The condition often involves chronic inflammation and recurrent infections, potentially requiring lifelong medical management.The severity can range from mild to severe, impacting lung function and overall health.
Example 1: A newborn infant presents with persistent cough, wheezing, and recurrent respiratory infections.Imaging studies reveal dilated bronchi, consistent with congenital bronchiectasis.Treatment focuses on infection control with antibiotics and bronchodilators., A child with cystic fibrosis develops progressive bronchiectasis.This secondary bronchiectasis is related to the underlying cystic fibrosis and requires specialized management addressing both conditions., A young adult with a history of congenital bronchiectasis experiences a severe exacerbation with significant respiratory compromise.Hospitalization for intravenous antibiotics and respiratory support is necessary.
Complete prenatal and postnatal history, including details of any respiratory symptoms.Imaging studies (chest X-ray, CT scan) to confirm the diagnosis and assess the extent of bronchiectasis. Pulmonary function tests to assess the severity of lung impairment. Records of any treatments, including antibiotics and bronchodilators. Documentation of infections and their management.
** The severity of congenital bronchiectasis is variable, and management strategies should be tailored to the individual's clinical presentation and response to treatment.Long-term follow-up is often necessary to monitor for complications and adjust treatment as needed.Genetic testing may be considered in some cases to identify any underlying genetic causes.
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