In simple words: This code describes a birth defect where the bile ducts, tubes that carry bile from the liver, are too narrow or blocked. This can cause problems with how the liver works and may lead to jaundice (yellowing of the skin and eyes).

This ICD-10-CM code classifies congenital stenosis and stricture of the bile ducts.It refers to a narrowing or constriction of the bile ducts present from birth. This condition can impede the flow of bile from the liver to the gallbladder and intestines, potentially causing jaundice, liver damage, and other complications. The diagnosis requires clinical evaluation, imaging studies (such as ultrasound or magnetic resonance cholangiopancreatography), and potentially liver function tests.

Example 1: A newborn infant presents with jaundice, elevated liver enzymes, and abdominal distension.Ultrasound reveals biliary duct stenosis. Code Q44.3 is assigned., A child with a history of recurrent cholangitis and elevated bilirubin levels undergoes magnetic resonance cholangiopancreatography (MRCP), revealing strictures in the bile ducts. Code Q44.3 is assigned., A teenager experiences progressive jaundice and abdominal pain, ultimately diagnosed with congenital bile duct stenosis through ERCP.Code Q44.3 is assigned.

Detailed clinical history, physical examination findings, relevant laboratory data (including liver function tests), and imaging studies (ultrasound, MRCP, ERCP as appropriate) are required to support the diagnosis and justify the use of Q44.3.

** Differential diagnosis should include other congenital biliary disorders such as biliary atresia, choledochal cysts, and Alagille syndrome.The clinical picture and imaging findings are critical in distinguishing these conditions.